in Late Diagnosed Congenital Hearing Loss with Delayed Speech: A Case Report

Authors

  • Muhammad Sobri Maulana Profesi Dokter, Fakultas Kedokteran Universitas Indonesi, Indonesia

DOI:

https://doi.org/10.31004/aulad.v3i3.73

Keywords:

Congenital hearing loss, Hearing Screening, Habilitation Strategy, Delayed Speech

Abstract

Introduction : Hearing impairment in children happened in 6 per 1000 newborn in developing country. The etiology of most of those case is unknown as stated by WHO that 60% of children hearing loss caused by genetics. Aim : This condition could lead to delayed speech in children. Method : A-6-years-old children referred to ENT department with delayed speech and bilateral profound sensorineural hearing loss to get a choclear implant. Result : Her condition suspected to be caused by rubella infection during pregnancy. She was already using hearing aid occasionaly and her mother complain that she still couldn’t hear effectively. The comprehensive management of infant with congenital hearing loss could be diagnosed early by applying hearing screening on all newborns at 1 month of age based on EHDI recommendation. This case represents the society low awareness and diagnostic tools limitation of congenital hearing loss prevention in Indonesia. Therefore, we suggest newborn hearing screening on all high-risked babies based on the risk factor stratification. Habilitation strategy for this patient includes auditory-verbal therapy. In order to maximize the benefit, parents are required to give maximum contribution to each therapy session. The therapy compliance becomes the important parameter in outcome optimization. Early diagnosis and intervention is the key to the management of congenital hearing loss. The EHDI programs provide recommended timeline for newborn hearing screenings, diagnostic examinations, and early interventions. The treatment consists of conventional hearing aid and cochlear implantation, combined with speech and language therapy in an appropriate educational environment, to promote development of communication and educational achievements

References

A, E.-B. (2004). Outcomes of Auditory-Verbal Therapy: A Review of the Evidence and a Call for Action. Volta Rev, 21—35.

Akinpelu OV, P. E. (2014). Otoacoustic emissions in newborn hearing screening: A systematic review of the effects of different protocols on test outcomes. Int J Pediatr Otorhinolaryngol, 711—717.

American Academy of Pediatrics, J. C. (2012). Principles and guidelines for early hearing detection and intervention programs. Pediatrics, 898—921.

Arumugam SV, P. V. (2015). Syndromic deafness-prevalence, distribution and hearing management protocol in Indian scenario. Annals of Medicine and Surgery 4. 143-150., 143-150.

audiology, A. a. (2020). American academy of audiology clinical practice guidelines: pediatric amplification American Speech-Language-Hearing Association. American academy of audiology.

Bond M, M. S. (2009). The effectiveness and cost-effectiveness of cochlear implants for severe to profound deafness in children and adults: a systematic review and economic model. Health Technol Assess Winch Engl, 1-330.

Chen MM, O. J. (2016). Diagnosis and management of congenital sensorineural hearing loss. . Curr Treat Options Pediatr, 256—265.

Chen Z, Y. D. (2009). Indications and common surgical approaches for cochlear implantation in China. ORL J Oto-Rhino-Laryngol Its Relat Spec, 187—191.

Cohen BE, D. A. (2014). Viral causes of hearing loss : a review for hearing health professionals. Trends in Hearing 2014, 1—17.

Dworsack-Dodge MM, G. J. (2012). Audiologic guidelines for the assessment of hearing in infants and young children. American Academy of Audiology.

Egilmez OK, K. M. (2015). Cochlear implant: indications, contraindications and complications. Scr Sci Medica, 9—16.

Force., U. P. (2002). Universal Screening for Hearing Loss in Newborns: US Preventive Services Task Force Hearing Screening: Costs of Establishing a Program. J Perinatol, 120—124.

Hearing, J. C. (2007). Year 2007 Position Statement: Principles and Guidelines for Early Hearing Detection and Intervention Programs. PEDIATRICS, 898—921.

Holster IL, H. L.-L. (2006). Evaluation of Hearing Loss after Failed Neonatal Hearing Screening. J Pediatr, 646—650.

Kaipa R, D. M. (2016). Efficacy of auditory- verbal therapy in children with hearing impairment: A systematic review from 1993 to 2015. Int J Pediatr Otorhinolaryngol, 124—134.

Kandogan T, D. A. (2013). Reliability of Auditory Steady-State Response (ASSR): Comparing Thresholds of Auditory Steady-State Response (ASSR) with Auditory Brainstem Response (ABR) in Children with Severe Hearing Loss. Indian J Otolaryngol Head Neck Surg, 604-607.

Khairi Md Daud M, N. R. ( 2010). The effect of mild hearing loss on academic performance in primary school children. Int J Pediatr Otorhinolaryngol, 67—70.

KR, W. (2004). Early hearing detection and intervention programs: opportunities for genetic services. Am J Med Genet A, 29—36.

L, C. (2009). Long-term follow-up of infants (4-11 months) fitted with cochlear implants. Acta Otolaryngol (Stockh). , 361—366.

Lieu JEC, T.-M. N. (2010). Unilateral hearing loss is associated with worse speech-language scores in children: a case-control study. Pediatrics, 1348—1355.

Lim SYC, S. J. (2005). Auditory-verbal therapy for children with hearing impairment. Ann Acad Med Singapore, 307—312.

Lin H-C, S. M.-T.-S.-M.-Y. (2015). Comparison of Hearing Screening Programs between One Step with Transient Evoked Otoacoustic Emissions (TEOAE) and Two Steps with TEOAE and Automated Auditory Brainstem Response. The Laryngoscope, 1957-1962.

Maulana, M. S. (2018). Effectiveness of Starting Weaning at 4 Months Compared to 6 Months to Reduce Anemia among Infants: An Evidence-Based Case Report. . World Nutrition Journal, 32.

Maulana, M. S. (2020). HUBUNGAN PENGASUHAN DI TEMPAT PENITIPAN TERHADAP PERKEMBANGAN PSIKOMOTOR, SOSIAL DAN BAHASA PADA ANAK USIA 1-5 TAHUN DI TPA AL IRSYAD TERNATE 2020. JECIES: Journal of Early Childhood Islamic Education Study, 79088.

Maulana, M. S. (2020). RISK OF LANGUAGE DELAY IN TODDLERS WITH PROLONGED SCREEN TIME : EVIDENCE BASED CASE REPOR. JECIES: Journal Of Early Childhood Islamic Education Study, 34-48.

Niparko JK, T. E.-Y. (2010). Spoken language development in children following cochlear implantation. JAMA, 1498—1506.

Olusanya BO, N. K. (2014). The global burden of disabling hearing impairment: a call to action. World Health Organ, 367—373.

Patel H, F. M. (2011). Universal newborn hearing screening. . Paediatr Child Health. , 301—305.

Peters JPM, R. G. (2016). Cochlear implantation in children with unilateral hearing loss: a systematic review. . The Laryngoscope, 713—721.

Porter HL, N. S. (2009). Using Benefit-Cost Ratio to Select Universal Newborn Hearing Screening Test Criteria. Ear Hear, 447—457.

Rahman MM, K. A. (2002). Congenital hearing impairment associated with rubella : lessons from Bangladesh. Southeast Asian J Trop Med Public Health, 811-817.

Reeder RM, C. J. (2015). Quantification of speech-in-noise and sound localisation abilities in children with unilateral hearing loss and comparison to normal hearing peers. Audiol Neurootol, 31—37.

Sampaio ALL, A. M. (2011). New criteria of indication and selection of patients to cochlear implant. Int J Otolaryngol.

Sininger YS, G. A. (2020). Auditory development in early amplified children: factors influencing auditory-based communication outcomes in children with hearing loss. . Ear Hear, 166—185.

Stevenson J, K. J. (2015). Emotional and behavioural difficulties in children and adolescents with hearing impairment: a systematic review and meta-analysis. Eur Child Adolesc Psychiatry, 477-496.

Tharpe AM, G. S. (2018). Management of children with mild, moderate, and moderately severe sensorineural hearing loss. Otolaryngol Clin North Am, 983—994.

Vincenti V, B. A. (2014). Pediatric cochlear implantation: an update. Ital J Pediatr, 40-72.

Walker EA, S. M. (2013). Predictors of hearing aid use time in children with mild-to-severe hearing loss. . Lang Speech Hear Serv Sch, 73—88.

Yoshinaga-Itano C, S. A. (1998). Language of early- and later-identified children with hearing loss. Pediatrics, 1161—1171.

Downloads

Published

2021-01-01

How to Cite

Maulana, M. S. (2021). in Late Diagnosed Congenital Hearing Loss with Delayed Speech: A Case Report. Aulad: Journal on Early Childhood, 3(3), 139–148. https://doi.org/10.31004/aulad.v3i3.73

Issue

Vol. 3 No. 3 (2020): December 2020

Section

Research Articles

Citation Check

License

Authors who publish with this journal agree to the following terms:

  • Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under  a Creative Commons Attribution-ShareAlike 4.0 International License  that allows others to share the work with an acknowledgement of the works authorship and initial publication in this journal.  
  • Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journals published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
  • Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access).